Rafizadeh Seyed Mohsen, Cheraqpour Kasra, Amoli Fahimeh Asadi, Haydar Ali A
Eye Research Center, Farabi Eye Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Ophthalmic Pathology Department, Farabi Eye Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Am J Ophthalmol Case Rep. 2022 Jul 3;27:101645. doi: 10.1016/j.ajoc.2022.101645. eCollection 2022 Sep.
Alveolar soft part sarcoma (ASPS) is a very rare type of soft tissue sarcomas which usually occurs in the limbs and trunk.
A 25-year-old woman presented with proptosis and redness of the right eye for 8-month. She suffered from severe right upper lid edema, conjunctival chemosis, downward displacement of the globe, and proptosis. Radiological imaging was nonconclusive. Histopathological evaluations confirmed ASPS. The patient underwent exenteration as a lifesaving procedure. At 16-month follow-up, the patient is stable without any signs of recurrence or metastasis.
We report an extremely rare case of ASPS occurring in the superior rectus muscle. Few orbital ASPS cases have been reported in the literature. A literature review of orbital ASPS was done to shed lights on the diagnosis and management of this rare tumor.
肺泡软部肉瘤（ASPS）是一种非常罕见的软组织肉瘤类型，通常发生于四肢和躯干。
一名25岁女性因右眼眼球突出和发红8个月就诊。她患有严重的右上睑水肿、结膜水肿、眼球下移和眼球突出。放射影像学检查结果不明确。组织病理学评估确诊为ASPS。为挽救生命，患者接受了眼眶内容剜除术。随访16个月时，患者病情稳定，无任何复发或转移迹象。
我们报告了一例极其罕见的发生于上直肌的ASPS病例。文献中报道的眼眶ASPS病例很少。对眼眶ASPS进行了文献综述，以阐明这种罕见肿瘤的诊断和治疗。
