Barre P S, Keith M W, Sobel M, Rashad F A, Shields R W
J Hand Surg Am. 1987 May;12(3):401-5. doi: 10.1016/s0363-5023(87)80013-8.
The presence of Okihiro's syndrome (congenital thenar hypoplasia and Duane's anomaly) in a patient became clinically significant when a hypothenar hammer syndrome developed. The ulnar artery occlusion resulted in a compromise of the hand's vascular supply because of a congenital hypoplastic radial artery. Resection of the thrombosed ulnar artery and insertion of an interposition vein graft restored circulation to the hand. Anatomic features in this case include a hypoplastic radial artery and double motor branch of the median nerve. Clinicians should consider Okihiro's syndrome in the differential diagnosis of thenar muscle atrophy since there are genetic, diagnostic, and clinical implications.
一名患有冈本综合征(先天性大鱼际发育不全和杜安氏异常)的患者,当发生小鱼际锤状指综合征时,该综合征的存在具有了临床意义。尺动脉闭塞导致手部血管供应受损,原因是先天性发育不全的桡动脉。切除血栓形成的尺动脉并插入一段静脉移植血管,恢复了手部的血液循环。该病例的解剖学特征包括发育不全的桡动脉和正中神经的双运动支。由于存在遗传、诊断和临床意义,临床医生在诊断大鱼际肌萎缩的鉴别诊断中应考虑冈本综合征。