Vijaya ENT Care Centre, Superspeciality Otology Centre, Bangalore, India.
University of Illinois-Chicago, Illinois, USA.
J Int Adv Otol. 2022 Jul;18(4):315-319. doi: 10.5152/iao.2022.21498.
The aim of this study was to classify congenital cholesteatoma along an entire spectrum of involvement ranging from the middle ear to petrous apex.
A total of 131 patients (85 adults and 46 children) underwent operations for congenital cholesteatoma over the duration of 27 years.
For most cases, middle ear mucosa was normal, the first ossicle eroded by the mass was the stapes, and the mastoid air cell system was well-pneumatized on intraoperative and radiographic views. Totally 34% of patients presented with facial nerve weakness and 45% of these cholesteatomas arose from the supralabyrinthine area (32.8%) and from the petrous apex (12.2%).
In this unified classification system, the otologist sees congenital cholesteatoma as a continuum, with facial nerve involvement and anacusis as part of the picture. This system of congenital cholesteatoma accommodates the supralabyrinthine and petrous bone locations of the disease.
本研究旨在对累及中耳至岩尖整个范围的先天性胆脂瘤进行分类。
27 年间，共有 131 例（85 例成人和 46 例儿童）先天性胆脂瘤患者接受了手术治疗。
大多数情况下，中耳黏膜正常，被肿块侵蚀的第一块听小骨是镫骨，术中及影像学检查均显示乳突气房系统充气良好。34%的患者出现面神经无力，其中 45%的胆脂瘤起源于上鼓室区（32.8%）和岩尖（12.2%）。
在这个统一的分类系统中，耳科医生将先天性胆脂瘤视为一个连续体，面神经受累和耳聋是其表现的一部分。该先天性胆脂瘤分类系统包括了上鼓室和岩尖骨的病变部位。
