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初诊时表现为下腔静脉平滑肌肉瘤伴肝转移的年轻男性:一个具有挑战性的诊断难题。

Inferior vena cava leiomyosarcoma with liver metastasis at presentation in a young male: A challenging diagnostic quandary.

机构信息

Department of Pathology, National Cancer Institute, Nagpur, Maharashtra, India.

Department of Radiology, National Cancer Institute, Nagpur, Maharashtra, India.

出版信息

Indian J Pathol Microbiol. 2022 Jul-Sep;65(3):686-688. doi: 10.4103/ijpm.ijpm_296_21.

Abstract

Leiomyosarcomas of vascular origin are very rare tumors, predominantly affecting the inferior vena cava (IVC). Although vascular leiomyosarcomas are slow-growing, their non-specific and late presentation results in delayed diagnosis which portends a very poor prognosis. Here we report a case of a 24-year-old man who presented with abdominal pain since 15 days and was found to have unresectable metastatic leiomyosarcoma of the inferior vena cava at initial diagnosis.

摘要

血管源性平滑肌肉瘤非常罕见,主要累及下腔静脉(IVC)。尽管血管平滑肌肉瘤生长缓慢,但因其表现无特异性且较晚,导致诊断延迟,预后极差。本文报告 1 例 24 岁男性,因腹痛 15 天就诊,初诊时发现下腔静脉不可切除转移性平滑肌肉瘤。

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