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男性泄殖腔样畸形:两例报告

Cloaca-Like Anomalies in the Male: A Report on Two Cases.

作者信息

AbouZeid Amr AbdelHamid, Mohammad Shaimaa Abdelsattar, Sos Marco Rady, Guirguis Nader Nassef, Mahmoud Heba A, El-Mahdy Manal

机构信息

Department of Pediatric Surgery, Ain Shams University, Cairo, Egypt.

Department of Radiodiagnosis, Ain Shams University, Cairo, Egypt.

出版信息

European J Pediatr Surg Rep. 2022 Jul 27;10(1):e93-e97. doi: 10.1055/s-0042-1750409. eCollection 2022 Jan.

Abstract

"Cloaca" is a term used to describe an anomaly in the female where a single orifice is located in the perineum draining both urogenital and gastrointestinal tracts. Few reports used the same term "cloaca" to describe the counterpart anomaly in the male. We present two "male" cases of anorectal anomalies associated with significant penile deformity (caudally displaced penis) that were managed during the period between January 2010 and September 2021. Characteristically, both cases had a single "central" perineal orifice. The latter was located anterior to the predestined site of the normal anus and just beneath a caudally positioned hypospadiac phallus. The caudal displacement of the penis was strikingly obvious by the presence of severe form of penoscrotal transposition. Both cases were associated with a perineal swelling (hamartoma) just beside the central perineal orifice. The urethra was very short (like that in the female), besides the single perineal orifice, which makes the presentation very similar to cloacal anomalies.

摘要

“泄殖腔”是一个用于描述女性异常情况的术语,即会阴处有一个单一开口,同时排泄泌尿生殖道和胃肠道。很少有报告使用相同的术语“泄殖腔”来描述男性的类似异常情况。我们呈现两例在2010年1月至2021年9月期间处理的与严重阴茎畸形(阴茎尾侧移位)相关的肛门直肠畸形“男性”病例。其特征是,两例均有一个单一的“中央”会阴开口。该开口位于正常肛门预定位置的前方,恰好在尾侧移位的尿道下裂阴茎下方。阴茎的尾侧移位因严重的阴茎阴囊转位而极为明显。两例均伴有中央会阴开口旁的会阴肿胀(错构瘤)。除了单一的会阴开口外,尿道非常短(类似于女性),这使得临床表现与泄殖腔畸形非常相似。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/09dc/9329137/39b2c2302267/10-1055-s-0042-1750409-i210633cr-1.jpg

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引用本文的文献

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J Indian Assoc Pediatr Surg. 2024 Jul-Aug;29(4):319-328. doi: 10.4103/jiaps.jiaps_30_24. Epub 2024 Jul 6.

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