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法洛四联症合并一种罕见类型的部分性肺静脉异位连接及左位心房总静脉。

Tetralogy of Fallot associated with a rare type partially anomalous pulmonary venous connection and levoatrial cardinal vein.

作者信息

Shin Ju A, Kang Nu-Ri, Lee Won Y

机构信息

Department of Pediatrics, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Republic of Korea.

Department of Clinical Korean Medicine, Graduate School, Kyung Hee University, Seoul, Republic of Korea.

出版信息

J Card Surg. 2022 Nov;37(11):3943-3946. doi: 10.1111/jocs.16825. Epub 2022 Aug 2.

DOI:10.1111/jocs.16825
PMID:35916159
Abstract

Tetralogy of Fallot is rarely associated with partially anomalous pulmonary venous connection. Unidentified partially anomalous pulmonary venous connection, however, might increase the risk of pulmonary valve replacement in repaired tetralogy of Fallot patients. Here, we present a case of a 19-year-old male who received a correction of tetralogy of Fallot 18 years ago and a rare type of partially anomalous pulmonary venous connection with levoatrial cardinal vein was identified during the follow-up period. The anomalous pulmonary veins were connected to the left hepatic vein and the right superior caval vein. Performing a pulmonary valve replacement, partially anomalous pulmonary venous connection was also corrected with a new approach using the venous plexus between the hepatic veins.

摘要

法洛四联症很少与部分性肺静脉异位连接相关。然而,未被识别的部分性肺静脉异位连接可能会增加法洛四联症修复术后患者进行肺动脉瓣置换的风险。在此,我们报告一例19岁男性患者,其18年前接受了法洛四联症矫治术,在随访期间发现了一种罕见的部分性肺静脉异位连接类型,即左房总静脉异位连接。异常肺静脉连接至左肝静脉和右上腔静脉。在进行肺动脉瓣置换时,还采用了一种利用肝静脉之间静脉丛的新方法纠正了部分性肺静脉异位连接。

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