Shri Bhagwan Mahavir Vitreoretina Services, Medical Research Foundation, Sankara Nethralaya, Chennai, Tamil Nadu, India.
Indian J Ophthalmol. 2022 Aug;70(8):3167. doi: 10.4103/ijo.IJO_1161_22.
A 40-year-old male presented with a complaint of sudden onset diminution of vision in the left eye for 2 weeks. He was a follow-up case with retinal hemangioblastoma in both eyes. He underwent two sittings of fundus fluorescein angiography-guided trans-pupillary thermotherapy 2 years back. Since then, he was regularly followed up for 2 years with stable vision and stable retinal findings. At present, the best-corrected visual acuity (BCVA) in the right eye is 6/6, and in the left eye, it is counting fingers 2 meters. On fundus examination, he had one active hemangioblastoma in the right eye and total retinal detachment in the left eye with multiple active lesions. The right eye was treated with a single sitting of thermotherapy, and the left eye underwent pars plana vitrectomy and angioma excision, followed by silicone oil tamponade. The immediate and late post-operative periods were uneventful, with successful anatomical and functional outcomes. The left eye BCVA on late follow-up was 6/36, no further treatment was advised, and the patient was kept under follow-up and observed closely.
: To educate regarding the systemic workup, diagnosis, and surgical management of complicated retinal detachment in retinal hemangioblastoma.
: Systemic workup, diagnosis, and surgical steps in the management of complicated retinal detachment in retinal hemangioblastoma were performed.
: Close follow-up, keen observation, and prompt treatment in the early stages of the disease are indispensable to prevent untoward sequelae of retinal hemangioblastoma. A thorough systemic workup is necessary to diagnose the systemic involvements early. Surgery, if indicated for the retinal hemangioblastoma or its associated sequelae, should be performed diligently and with careful handling of blood vessels and anomalous tissues.
一名 40 岁男性因左眼突发性视力下降 2 周就诊。他是双眼视网膜血管瘤的复诊病例。他在 2 年前接受了 2 次眼底荧光素血管造影引导的经瞳孔温热疗法。此后，他定期随访 2 年，视力和视网膜情况稳定。目前，右眼最佳矫正视力（BCVA）为 6/6，左眼为 2 米指数。眼底检查发现右眼有一个活跃的血管瘤，左眼完全视网膜脱离，并有多个活跃病变。右眼接受了单次热疗，左眼接受了经睫状体平坦部玻璃体切除术和血管瘤切除术，随后进行硅油填充。即刻和晚期术后均无并发症，解剖和功能结果均成功。左眼晚期随访时的 BCVA 为 6/36，无需进一步治疗，建议继续随访观察。
教育关于视网膜血管瘤复杂视网膜脱离的系统检查、诊断和手术治疗。
对视网膜血管瘤复杂视网膜脱离的系统检查、诊断和手术步骤进行了阐述。
密切随访、敏锐观察和早期疾病的及时治疗对于预防视网膜血管瘤的不良后果至关重要。彻底的系统检查对于早期诊断全身受累是必要的。如果需要手术治疗视网膜血管瘤或其相关并发症，应谨慎处理血管和异常组织。
