Kılıç Şahhan, Çınar Tufan, Çiçek Vedat, Asal Suha, Selçuk Murat, Keskin Muhammed, Güner Mehtap, Turan Ahmet, Orhan Ahmet Lütfullah
Haydarpasa Sultan Abdülhamid Han Training and Research Hospital, Health Sciences University, Istanbul, Turkey.
J Tehran Heart Cent. 2021 Oct;16(4):178-181. doi: 10.18502/jthc.v16i4.8605.
Intravenous leiomyomatosis (IVL) is a rare and benign smooth muscle tumor that arises from intrauterine venules or the myometrium. We herein describe a 49-year-old woman with a history of myomectomy who developed abdominal pain. An intravascular mass with extension to the right atrium was detected in the inferior vena cava. The mass was surgically resected in a single stage under cardiopulmonary bypass. IVL features were indicated by subsequent histopathology. Postoperatively, the patient was diagnosed with massive pericardial effusion and treated with a pericardial window. At 3 months' outpatient clinical follow-up, she was asymptomatic. This case indicates that the diagnosis of IVL with extension to the heart should be kept in mind in patients presenting with abdominal pain.
静脉内平滑肌瘤病(IVL)是一种罕见的良性平滑肌肿瘤,起源于子宫内小静脉或子宫肌层。我们在此描述一名49岁有子宫肌瘤切除术史的女性,她出现了腹痛。在下腔静脉中检测到一个延伸至右心房的血管内肿块。在体外循环下对该肿块进行了一期手术切除。随后的组织病理学显示具有IVL特征。术后,患者被诊断为大量心包积液,并接受了心包开窗术治疗。在门诊临床随访3个月时,她没有症状。该病例表明,对于出现腹痛的患者,应考虑到IVL延伸至心脏的诊断。