气管原发性腺样囊性癌：慢性呼吸困难的隐匿性诊断。
Primary adenoid cystic carcinoma of the trachea: an elusive diagnosis of chronic dyspnoea.
机构信息
Department of Medical Oncology, Instituto Português de Oncologia de Coimbra Francisco Gentil EPE, Coimbra, Portugal
Department of Pathology, Hospital de Santa Maria, Lisboa, Portugal.
出版信息
BMJ Case Rep. 2022 Aug 9;15(8):e250227. doi: 10.1136/bcr-2022-250227.
Primary adenoid cystic carcinoma (ACC) of the trachea is a rare entity, with a 5-year survival between 50% and 80% for resectable cases and 30% in case of unresectable disease. We report a case of a primary ACC on a woman in her 70s that presented with a drawn-out history of dyspnoea. She was diagnosed with an unresectable obstructive tumour of the trachea, which required the placement of a Y-shaped stent. The patient underwent concomitant chemoradiotherapy, with partial response, and is still in follow-up, without evidence of disease progression.
气管原发性腺样囊性癌（ACC）较为罕见，可切除病例的 5 年生存率为 50%至 80%，不可切除病例的生存率为 30%。我们报告了一例 70 多岁女性的原发性 ACC 病例，该患者有长时间的呼吸困难病史。她被诊断为不可切除的气管阻塞性肿瘤，需要放置 Y 形支架。患者接受了同期放化疗，部分缓解，目前仍在随访中，无疾病进展迹象。
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