Freeman B H, Bray E W, Meyer L C
J Bone Joint Surg Am. 1987 Jun;69(5):691-8.
Involvement of the proximal part of the femur by polyostotic fibrous dysplasia is a progressive and disabling condition that leads to deformity. Morbidity is high in terms of recurrent fracture and deformity. Conventional methods of treatment have been ineffective in controlling these problems. The cases of four patients were reviewed to determine the natural history of polyostotic fibrous dysplasia involving the proximal part of the femur. In six femora, multiple osteotomies with fixation using a Zickel nail was utilized to provide definitive control of deformity and recurrent fracture and to allow the patients to return to normal activities.
多骨型纤维结构不良累及股骨近端是一种进行性致残疾病，可导致畸形。就复发性骨折和畸形而言，发病率很高。传统治疗方法在控制这些问题方面一直无效。回顾了4例患者的病例，以确定多骨型纤维结构不良累及股骨近端的自然病程。在6个股骨中，采用多段截骨并用Zickel钉固定，以明确控制畸形和复发性骨折，并使患者能够恢复正常活动。
