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复发性多软骨炎伴孤立性气管支气管受累并合并干燥综合征：一例报告

Relapsing polychondritis with isolated tracheobronchial involvement complicated with Sjogren's syndrome: A case report.

作者信息

Chen Jun-Yan, Li Xiao-Yan, Zong Chen

机构信息

Department of Pulmonary and Critical Care Medicine, The Second Hospital of Shanxi Medical University, Taiyuan 030000, Shanxi Province, China.

出版信息

World J Clin Cases. 2022 Jul 6;10(19):6563-6570. doi: 10.12998/wjcc.v10.i19.6563.

DOI:10.12998/wjcc.v10.i19.6563
PMID:35979285
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9294918/
Abstract

BACKGROUND

Relapsing polychondritis (RP) is a rare, long-term, and potentially life-threatening disease characterised by recurrent paroxysmal inflammation that can involve and destroy the cartilage of the external ear, nose, larynx, and trachea.

CASE SUMMARY

We here report a case of RP involving solely the tracheobronchial cartilage ring (and not the auricular. nasal or articular cartilage) complicated by Sjögren's syndrome in a 47-year-old female whose delayed diagnosis caused a sharp decline in pulmonary function. After corticosteroid treatment, her pulmonary function improved.

CONCLUSION

In such cases, our experience suggested that 18F-fluorodeoxyglucose positron emission tomography/computed tomography (18F-FDG PET/CT) and fiberoptic bronchoscopy should be used to diagnose airway chondritis as relapsing polychondritis in the early phase of disease.

摘要

背景

复发性多软骨炎（RP）是一种罕见的、长期的、可能危及生命的疾病，其特征为反复发作的阵发性炎症，可累及并破坏外耳、鼻、喉和气管的软骨。

病例摘要

我们在此报告一例仅累及气管支气管软骨环（而非耳廓、鼻或关节软骨）的复发性多软骨炎病例，该病例发生于一名47岁女性，并发干燥综合征，其延迟诊断导致肺功能急剧下降。经皮质类固醇治疗后，她的肺功能得到改善。

结论

在这类病例中，我们的经验表明，应使用18F-氟脱氧葡萄糖正电子发射断层扫描/计算机断层扫描（18F-FDG PET/CT）和纤维支气管镜在疾病早期诊断气道软骨炎为复发性多软骨炎。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/8f2a75f3453f/WJCC-10-6563-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/0fb8df7577a0/WJCC-10-6563-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/ac9cbcfdbc88/WJCC-10-6563-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/da7fe23e1867/WJCC-10-6563-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/e211086b133c/WJCC-10-6563-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/b8673b2f30bf/WJCC-10-6563-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/8f2a75f3453f/WJCC-10-6563-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/0fb8df7577a0/WJCC-10-6563-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/ac9cbcfdbc88/WJCC-10-6563-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/da7fe23e1867/WJCC-10-6563-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/e211086b133c/WJCC-10-6563-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/b8673b2f30bf/WJCC-10-6563-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6bc1/9294918/8f2a75f3453f/WJCC-10-6563-g006.jpg

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A 49-Year-Old Man Presents With Fever of Unknown Origin and Cough.一位 49 岁男性因不明原因发热和咳嗽就诊。
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