疑似家族性低钾性麻痹导致的印度尼西亚成年人急性弛缓性麻痹：一例罕见病例。

Acute flaccid paralysis in Indonesian adult due to suspected familial hypokalemia paralysis: A rare case.

作者信息

Aprinda Devani Bagus, Suryantoro Satriyo Dwi

机构信息

Department of Internal Medicine, Faculty of Medicine, Universitas Airlangga, Surabaya, Indonesia.

Kaliwates General Hospital, Jember, Indonesia.

出版信息

Ann Med Surg (Lond). 2022 Aug 4;80:104329. doi: 10.1016/j.amsu.2022.104329. eCollection 2022 Aug.

DOI:10.1016/j.amsu.2022.104329

PMID:36045796

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9422396/

Abstract

BACKGROUND

Familial hypokalemic periodic paralysis (FHPP) is rare, so its management is essential to report.

CASE PRESENTATION

A 25-year-old Indonesian woman complained of feeling weak in both hands and legs, but the heaviest in both legs. The patient has several family members with similar complaints. The patient experienced decreased muscle strength in the upper extremity of 4/4 and the lower extremity of 3/3. Laboratory investigation showed potassium of 2.0 mmol/L, and the patient was given KCL of 50 mEq/24 hours, KSR of 3 × 600 mg/24 hours for 3 days, and a high potassium diet. The next few days, potassium levels increased, and the patient was treated as an outpatient.

DISCUSSION

Early diagnosis and management of acute flaccid paralysis (AFP) due to FHPP are very effective in low-resource settings.

CONCLUSION

Finding the cause of AFP is essential for better management.

摘要

背景

家族性低钾性周期性麻痹（FHPP）较为罕见，因此报告其治疗情况至关重要。

病例介绍

一名25岁的印度尼西亚女性主诉双手和双腿无力，尤以双腿最为严重。该患者有几名家庭成员也有类似症状。患者上肢肌力下降至4/4，下肢肌力下降至3/3。实验室检查显示血钾为2.0 mmol/L，给予患者24小时静脉输注50 mEq氯化钾、连续3天每天口服3次每次600 mg枸橼酸钾，并采用高钾饮食。接下来的几天里，血钾水平上升，患者转为门诊治疗。