Martins Ana, Pimenta Sofia, Rato Maria, Oliveira Daniela, Martins Frederico Rajão, Pinheiro Filipe Oliveira, Fonseca Diogo, Costa Lúcia
Rheumatology, Centro Hospitalar Universitário São João, Porto, Portugal.
Rheumatology, University Hospital Center of Algarve, Faro, Portugal.
ARP Rheumatol. 2022 Jul 21.
Serositis is seen in approximately 12% of patients with systemic lupus erythematosus (SLE), usually in the form of pleuritis or pericarditis. Peritoneal serositis with ascites is an extremely rare manifestation of SLE and ascites as initial manifestation of SLE is even rarer. Here, we describe a previously healthy 48-year-old female with periumbilical abdominal pain, constitutional symptoms, ascites, pleural effusions and raised CA-125 level as an initial manifestation of SLE, which led up to the diagnosis of pseudo-pseudo Meigs syndrome. PPMS is a rare manifestation of SLE and awareness of this entity among clinicians is crucial to ensure an early recognition and prompt treatment.
浆膜炎见于约12%的系统性红斑狼疮(SLE)患者,通常表现为胸膜炎或心包炎。伴有腹水的腹膜浆膜炎是SLE极为罕见的表现,而腹水作为SLE的初始表现则更为罕见。在此,我们描述了一名既往健康的48岁女性,以脐周腹痛、全身症状、腹水、胸腔积液和CA-125水平升高作为SLE的初始表现,最终诊断为假性梅格斯综合征。假性梅格斯综合征是SLE的罕见表现,临床医生了解这一实体对于确保早期识别和及时治疗至关重要。