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晕厥性肉瘤:原发性心脏滑膜肉瘤的罕见病例

The Syncopal Sarcoma: A Rare Case of Primary Cardiac Synovial Sarcoma.

作者信息

Eqbal Adam J, Goodliffe Laura, Masoom Hassan, Ajlan Muhammad, Hanna Jessica, Vukmirovic-Popovic Snezana, Philips Ashwin, Belley-Côté Emilie P, Salehian Omid, Whitlock Richard P

机构信息

Division of Cardiac Surgery, McMaster University, Hamilton, Ontario, Canada.

Division of Cardiology, McMaster University, Hamilton, Ontario, Canada.

出版信息

JACC Case Rep. 2022 Aug 17;4(16):1037-1041. doi: 10.1016/j.jaccas.2022.07.010.

DOI:10.1016/j.jaccas.2022.07.010
PMID:36062056
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9434647/
Abstract

Primary cardiac synovial sarcomas are very rare, representing <1% of all primary cardiac tumors. We report the case of a 19-year-old man with syncope and dynamic obstructive shock caused by a large right-sided intracardiac tumor. ( ).

摘要

原发性心脏滑膜肉瘤非常罕见,占所有原发性心脏肿瘤的比例不到1%。我们报告了一例19岁男性患者,因右侧心腔内巨大肿瘤导致晕厥和动态梗阻性休克。( )

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/902319ff2b45/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/5bbbf948d66c/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/242bdf5fddf5/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/8e6505b9cba8/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/f7490a14cfc6/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/9890a1a82005/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/902319ff2b45/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/5bbbf948d66c/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/242bdf5fddf5/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/8e6505b9cba8/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/f7490a14cfc6/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/9890a1a82005/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9891/9434647/902319ff2b45/gr5.jpg

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引用本文的文献

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Primary cardiac sarcoma: demographics, genomic study correlation, and survival benefits of surgery with adjuvant therapy in U.S. population.原发性心脏肉瘤:美国人群的人口统计学、基因组研究相关性以及手术联合辅助治疗的生存获益。
Clin Res Cardiol. 2024 May;113(5):694-705. doi: 10.1007/s00392-023-02236-x. Epub 2023 May 29.

本文引用的文献

1
Incidence, prognostic significance, and survival outcomes of primary cardiac sarcoma: An updated population-based retrospective study.原发性心脏肉瘤的发病率、预后意义和生存结局:一项基于人群的更新回顾性研究。
Anatol J Cardiol. 2021 Feb;25(2):104-110. doi: 10.14744/AnatolJCardiol.2020.78107.
2
The prognostic impact of SYT-SSX fusion type and histological grade in pediatric patients with synovial sarcoma treated according to the CWS (Cooperative Weichteilsarkom Studie) trials.根据CWS(儿童软组织肉瘤协作研究)试验治疗的小儿滑膜肉瘤患者中,SYT-SSX融合类型和组织学分级的预后影响。
Pediatr Blood Cancer. 2017 Jan;64(1):89-95. doi: 10.1002/pbc.26206. Epub 2016 Sep 13.
3
National trends in resource utilization associated with ED visits for syncope.
与晕厥急诊就诊相关的资源利用的全国趋势。
Am J Emerg Med. 2015 Aug;33(8):998-1001. doi: 10.1016/j.ajem.2015.04.030. Epub 2015 Apr 24.
4
Primary cardiac synovial sarcoma.原发性心脏滑膜肉瘤。
Ann Thorac Surg. 2013 Jun;95(6):2202-9. doi: 10.1016/j.athoracsur.2013.01.030. Epub 2013 May 3.
5
Syncope.晕厥
Circulation. 2013 Mar 26;127(12):1330-9. doi: 10.1161/CIRCULATIONAHA.112.138396.