Holm-Weber Thomas, Gjedsted Jacob, Schmidt Michael Rahbek, Helvind Morten, Hjortdal Vibeke E
Thoraxkirurgisk Klinik, Københavns Universitetshospital - Rigshospitalet.
Thoraxanæstesiologisk Klinik, Københavns Universitetshospital - Rigshospitalet.
Ugeskr Laeger. 2022 Aug 15;184(33).
Protein-losing enteropathy (PLE) is a severe Fontan complication. This is a case report of the first hybrid treatment of PLE in Denmark of an 11-year-old Fontan patient with severe symptoms (diarrhoea, fatigue and swelling) and low albumin level. Diagnostics included intranodal and intrahepatic dynamic contrast magnetic resonance lymphangiography. The hybrid intervention consisted of selective lymphatic duct embolisation and innominate vein turn-down to treat PLE. The interventions went well, and two months after discharge the patient was relieved from PLE symptoms, the albumin level was normalised, and the patient felt more energetic.
蛋白丢失性肠病（PLE）是一种严重的Fontan并发症。本文报告了丹麦首例对一名11岁患有严重症状（腹泻、疲劳和肿胀）且白蛋白水平低的Fontan患者进行PLE混合治疗的病例。诊断方法包括结内和肝内动态对比磁共振淋巴管造影。混合干预措施包括选择性淋巴管栓塞和无名静脉折返术以治疗PLE。干预进展顺利，出院两个月后患者的PLE症状得到缓解，白蛋白水平恢复正常，且患者感觉精力更充沛。
