Jamaer C, Berquin C, Sinatti C, Schechter M Y, Wolff D T, van Laecke E, Hoebeke P, Spinoit A F
Department of Urology, Ghent University Hospital, ERN EUROGEN Accredited Centre, Belgium.
Department of Urology, Ghent University Hospital, ERN EUROGEN Accredited Centre, Belgium.
J Pediatr Urol. 2022 Oct;18(5):706-707. doi: 10.1016/j.jpurol.2022.08.008. Epub 2022 Aug 19.
Duplication of the urethra is a rare congenital anomaly in females which, if left unidentified, might cause refractory urinary incontinence. This video demonstrates its identification and treatment.
PATIENT & METHODS: A 5-year-old female was referred for primary refractory diurnal incontinence without any dry moment since birth. Initial clinical examination showed permanent urine leakage from an opening cranial to the clitoris. Ultrasound did not show any bladder or kidney abnormalities. A diagnostic cystoscopy under anesthesia revealed an accessory meatus located cranially to the orthotopic meatus and to the clitoris.
Lying in dorsal decubitus under general anesthesia, catheters were inserted in respectively the orthotopic and accessory meatus. The accessory meatus and urethra were dissected away into the bladder dome from a circumferential skin incision. Defects were closed and bladder drainage per urethram was left in situ for 10 days. P ostoperative recovery was uncomplicated. Complete resolution of the incontinence was immediately achieved at catheter removal. Daytime and night-time continence are observed with 3 years follow-up.
Urethral duplication is a rare finding in females but should be excluded during the workup of primary incontinence. In girls with isolated urethral duplication, resection of the accessory urethra is the best surgical option.
女性尿道重复是一种罕见的先天性异常,如果未被识别,可能导致难治性尿失禁。本视频展示了其识别与治疗方法。
一名5岁女性因原发性难治性日间尿失禁前来就诊,自出生以来无任何干爽时刻。初步临床检查显示,在阴蒂上方的一个开口处持续漏尿。超声检查未发现膀胱或肾脏有任何异常。麻醉下的诊断性膀胱镜检查显示,在正常尿道口及阴蒂上方存在一个副尿道口。
在全身麻醉下取仰卧位,分别将导管插入正常尿道口和副尿道口。从环形皮肤切口将副尿道口及尿道向膀胱穹窿部游离并切除。关闭缺损部位,经尿道留置膀胱引流管10天。术后恢复顺利。拔除导管后立即实现尿失禁完全缓解。随访3年,观察到患者日间和夜间均能自主控制排尿。
女性尿道重复较为罕见,但在原发性尿失禁的检查过程中应予以排除。对于孤立性尿道重复的女孩,切除副尿道是最佳手术选择。