O'Brien D M, Ghent W R, Dexter D F
Can J Surg. 1987 Jul;30(4):277-9.
Cutaneous hemangiomas are frequently found on routine clinical examination and generally are not important. But when internal organs are involved, these vascular tumours assume greater importance because of associated morbidity. A case is presented of multiple organ involvement by angiomas in a woman with a history of flank hemangioma who was investigated for hematuria and splenomegaly. She subsequently underwent splenectomy. The uncommon systemic syndromes characterized by vascular tumours are discussed, and the case reported is appropriately classified. The clinical picture, pathologic features and investigations appropriate for systemic cystic angiomatosis are briefly reviewed. The authors recommend conservative management when there is splenic involvement unless the size of the spleen makes its rupture likely or when there are hematologic complications.
皮肤血管瘤在常规临床检查中经常被发现，一般来说并不重要。但当累及内脏器官时，这些血管肿瘤由于相关的发病率而变得更为重要。本文报告一例有侧腹血管瘤病史的女性患者，因血尿和脾肿大接受检查，发现血管瘤累及多个器官。她随后接受了脾切除术。文中讨论了以血管肿瘤为特征的罕见全身综合征，并对所报告的病例进行了恰当分类。简要回顾了系统性囊性血管瘤病的临床表现、病理特征及相关检查。作者建议，当脾脏受累时，除非脾脏大小可能导致破裂或存在血液学并发症，否则应采取保守治疗。
