Hematology Department, Hospital Clínico Universitario-INCLIVA, Valencia, Spain.
Department of Hemotherapy and Hemostasis, Hospital Clínic, Barcelona, Spain.
Br J Haematol. 2022 Nov;199(4):529-538. doi: 10.1111/bjh.18440. Epub 2022 Sep 12.
Available data have proved insufficient to develop consensus recommendations on the prevention of thrombosis and bleeding in myelofibrosis (MF). We evaluated the incidence and risk factors of vascular complications in 1613 patients from the Spanish Myelofibrosis Registry. Over a total of 6981 patient-years at risk, 6.4% of the study population had at least one thrombotic event after MF diagnosis, amounting to an incidence rate of 1.65 per 100 patient-years. Prior history of thrombosis, the JAK2 mutation, and the intermediate-2/high-risk International Prognostic Scoring System (IPSS) categories conferred an increased thrombotic risk after adjustment for the risk-modifying effect of anti-thrombotic and cytoreductive treatments. History of thrombosis and the JAK2 mutation allowed us to pinpoint a group of patients at higher risk of early thrombosis. No decreased incidence of thrombosis was observed while patients were on anti-thrombotic or cytoreductive treatment. An increased risk of venous thrombosis was found during treatment with immunomodulatory agents. A total of 5.3% of patients had at least one episode of major bleeding, resulting in an incidence rate of 1.5 events per 100 patient-years. Patients in the intermediate-2/high-risk IPSS categories treated with anti-coagulants had an almost sevenfold increased risk of major bleeding. These findings should prove useful for guiding decision-making in clinical practice.
现有数据不足以制定骨髓纤维化(MF)血栓和出血预防的共识建议。我们评估了西班牙骨髓纤维化登记处 1613 例患者的血管并发症发生率和危险因素。在总计 6981 患者年的风险中,研究人群中有 6.4%在 MF 诊断后至少发生了一次血栓事件,发生率为每 100 患者年 1.65 次。血栓形成史、JAK2 突变和中间 2/高危国际预后评分系统(IPSS)类别,在调整抗血栓和细胞减少治疗的风险修正作用后,增加了血栓形成风险。血栓形成史和 JAK2 突变使我们能够确定一组具有较高早期血栓形成风险的患者。在接受抗血栓和细胞减少治疗的患者中,并未观察到血栓形成发生率降低。在使用免疫调节药物治疗期间,静脉血栓形成的风险增加。共有 5.3%的患者至少发生过一次大出血事件,发生率为每 100 患者年 1.5 次。接受抗凝治疗的中间 2/高危 IPSS 类别的患者发生大出血的风险几乎增加了七倍。这些发现对于指导临床实践中的决策应该是有用的。