Sakabe Mitsukuni, Tobino Kazunori, Uchida Kazuki, Murakami Yosuke, Hiramatsu Yuri, Ota Hiroaki, Kawabata Takafumi
Department of Respiratory Medicine, Iizuka Hospital, 3-83 Yoshiomachi, Iizuka, Fukuoka, 820-0018, Japan.
Department of Respiratory Medicine, Juntendo University, School of Medicine, 2-1-1 Bunkyo-Ku, Hongo, 113-8421, Japan.
Respir Med Case Rep. 2022 Sep 6;39:101734. doi: 10.1016/j.rmcr.2022.101734. eCollection 2022.
We report a case of an isolated congenital interruption of the right interlobar pulmonary artery with unilateral interstitial lung abnormality. 3D-CT with enhancement showed absent right interlobar pulmonary artery without any other abnormalities of the pulmonary artery and an enlarged inferior phrenic artery. High-resolution CT demonstrated ground-glass opacities, reticular changes, and small cysts in the right middle and lower lobes, which were compatible with interstitial lung abnormality. The patient was diagnosed with an isolated congenital interruption of the right interlobar pulmonary artery since chronic pulmonary thromboembolism, structural heart disease, systemic congenital disease, and systemic vasculitis were ruled out.
我们报告一例孤立性先天性右肺叶间动脉中断合并单侧间质性肺异常的病例。增强三维CT显示右肺叶间动脉缺如，肺动脉无其他异常，膈下动脉增粗。高分辨率CT显示右中、下叶磨玻璃影、网状改变及小囊肿，符合间质性肺异常表现。由于排除了慢性肺血栓栓塞症、结构性心脏病、全身性先天性疾病和系统性血管炎，该患者被诊断为孤立性先天性右肺叶间动脉中断。
