Chen Zushun, Lu Haiming, Xu Jingxuan, Ma Liang
Hepatobiliary Surgery, Guangxi Medical University Cancer Hospital, Nanning, Guangxi, China.
Intractable Rare Dis Res. 2022 Aug;11(3):158-160. doi: 10.5582/irdr.2022.01076.
Cholangiocytic adenoma in the hilar bile duct is rare, and elevated IgG4 at the same time is extremely rare. This situation has not been reported in the literature. Nonetheless, the current case involved hilar biliary cystadenoma with elevated IgG4 levels. A 66-year-old man presented at this hospital with dark tea-colored urine. Preoperative imaging studies suggested hilar cholangiocarcinoma. This case demonstrates the difficulty of preoperative diagnosis of benign hilar lesions and the rarity of two combined benign lesions. A point of contention is whether this case should be treated with surgery or hormone therapy.
肝门部胆管的胆管细胞腺瘤罕见，同时IgG4升高极为罕见。这种情况在文献中尚未见报道。尽管如此，目前该病例为IgG4水平升高的肝门部胆管囊腺瘤。一名66岁男性因尿色如浓茶入住本院。术前影像学检查提示肝门部胆管癌。该病例显示了术前诊断良性肝门部病变的困难以及两种良性病变合并存在的罕见性。一个有争议的问题是该病例应采用手术治疗还是激素治疗。
