Weryński Piotr, Malinowska-Weryńska Agnieszka, Wójcik Agnieszka, Kołcz Jacek
Department of Pediatric Cardiology, Medical College in Cracow, Jagiellonian University, Kraków, Poland.
Ann Pediatr Cardiol. 2022 Mar-Apr;15(2):216-218. doi: 10.4103/apc.apc_266_20. Epub 2022 Aug 19.
Interrupted aortic arch (IAA) associated with an aortopulmonary window (APW) is a rare cardiac malformation that needs an immediate diagnosis after birth and surgical treatment to avoid irreversible pulmonary lesions. Herein, we describe a case of successful staged treatment of premature neonate using many operative procedures. The first stage was stenting of patent ductus arteriosus with banding of pulmonary artery branches using a hybrid approach. At the age of one, he underwent total correction of malformation using Gore-Tex patch. Two procedures of implantation and redilatation of the previously implanted stents were performed in the following years. In the 8-year follow-up, the patient has been in good clinical condition, without cardiac symptoms. To the best of our knowledge, this is the first case report representing such a long-term follow-up of treatment of IAA accompanied by APW.
主动脉弓中断(IAA)合并主肺动脉窗(APW)是一种罕见的心脏畸形,出生后需要立即诊断并进行手术治疗,以避免不可逆的肺部病变。在此,我们描述了一例早产新生儿通过多次手术成功进行分期治疗的病例。第一阶段采用杂交手术,对动脉导管进行支架置入并对肺动脉分支进行束带结扎。一岁时,他使用戈尔特斯(Gore-Tex)补片进行了畸形的完全矫正。在接下来的几年里,又进行了两次先前植入支架的植入和再扩张手术。在8年的随访中,患者临床状况良好,无心脏症状。据我们所知,这是首例对伴有APW的IAA治疗进行如此长期随访的病例报告。