Li Baofei, Wang Haiyang, Jiang Zheng, Wang Rui, Yang Jie, Chen Fei
Department of Otolaryngology, Head and Neck Surgery, West China Hospital, Sichuan University, Chengdu, China.
West China Hospital, Sichuan University, Chengdu, China.
Ear Nose Throat J. 2025 Mar;104(1_suppl):219S-223S. doi: 10.1177/01455613221135650. Epub 2022 Oct 19.
Angiosarcoma is a rare primary tracheal-bronchus origin tumor which was only reported in a few cases. The diagnosis and treatment for such a rare tumor has long been a challenge. In this case, a male hemoptysis patient who was initially misdiagnosed with thyroid carcinoma with tracheal invasion was finally diagnosed with tracheal angiosarcoma. A thick-walled cystic nodular mass was found preoperatively in the right thyroid lobe overlying the tracheal angiosarcoma, which contributed to our initial misdiagnosis. Flap bleeding and necrosis occured after the surgery and patient continued to cough blood even when we excised the whole flap, which suggested the intramural growth and local invasion of the angiosarcoma. This study also reviewed previous literactures on airway angiosarcoma and discussed the treatment strategy.
血管肉瘤是一种罕见的起源于气管支气管的原发性肿瘤，仅有少数病例报道。对于这种罕见肿瘤的诊断和治疗一直是一项挑战。在本病例中，一名最初被误诊为甲状腺癌侵犯气管的男性咯血患者最终被诊断为气管血管肉瘤。术前在覆盖气管血管肉瘤的右甲状腺叶发现一个厚壁囊性结节状肿块，这导致了我们最初的误诊。术后皮瓣出现出血和坏死，即使我们切除了整个皮瓣，患者仍持续咯血，这提示血管肉瘤的壁内生长和局部侵犯。本研究还回顾了以往关于气道血管肉瘤的文献并讨论了治疗策略。
