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假性特发性甲状旁腺功能减退症:1例报告及日本文献综述

Pseudoidiopathic hypoparathyroidism: report of a case and review of the literature in Japan.

作者信息

Nakano T, Masuoka H, Hamaguchi K, Takezawa H

出版信息

Jpn J Med. 1987 May;26(2):226-9. doi: 10.2169/internalmedicine1962.26.226.

DOI:10.2169/internalmedicine1962.26.226
PMID:3626163
Abstract

A case of pseudoidiopathic hypoparathyroidism is described. The patient, 47-year-old male, developed numbness and muscle spasms in the extremities in July 1980. Physical and laboratory examinations revealed positive Chvostek and Trousseau's signs, hypocalcemea, mild hyperphosphatemia, normal serum magnesium, prolongation of QTc on EKG, normal reaction to Ellsworth-Howard test and high levels of serum PTH. Treatment with calcium lactate and vitamin D was successful. The literature regarding 16 cases reported in Japan was reviewed.

摘要

本文描述了一例假性特发性甲状旁腺功能减退症病例。患者为47岁男性,于1980年7月出现四肢麻木和肌肉痉挛。体格检查和实验室检查显示,Chvostek征和Trousseau征阳性、低钙血症、轻度高磷血症、血清镁正常、心电图QTc延长、对埃尔斯沃思-霍华德试验反应正常以及血清甲状旁腺激素水平升高。乳酸钙和维生素D治疗取得成功。并对日本报道的16例相关文献进行了回顾。

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Jpn J Med. 1987 May;26(2):226-9. doi: 10.2169/internalmedicine1962.26.226.
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