Khan Usman A, Plonsker Jillian H, Friedman Rick A, Schwartz Marc S
Department of Neurosurgery and.
Division of Head and Neck Surgery, University of California San Diego, California.
Neurosurg Focus Video. 2021 Oct 1;5(2):V17. doi: 10.3171/2021.7.FOCVID21130. eCollection 2021 Oct.
The natural history of neurofibromatosis type 2 (NF2) is profound bilateral hearing loss. The decision to pursue microsurgery may be more complicated in NF2 than with sporadic tumors. Schwannomas in NF2 often occur with other skull base tumors. Treatment should be tailored to preserve auditory perception for as long as possible. The authors present the case of a man with NF2 and a vestibular schwannoma who has poor hearing on the same side as a large petrous apex meningioma, both opposite to a well-hearing ear. This case highlights surgical decision-making and technical nuances during resection of collision tumors in NF2. The video can be found here: https://stream.cadmore.media/r10.3171/2021.7.FOCVID21130.
2型神经纤维瘤病(NF2)的自然病程是严重的双侧听力丧失。与散发性肿瘤相比,NF2患者进行显微手术的决策可能更为复杂。NF2中的神经鞘瘤常与其他颅底肿瘤同时出现。治疗应进行调整,以尽可能长时间地保留听觉。作者介绍了一例患有NF2和前庭神经鞘瘤的男性病例,其听力差的一侧同时存在一个巨大的岩尖脑膜瘤,而听力良好的耳朵则在对侧。该病例突出了NF2中碰撞肿瘤切除过程中的手术决策和技术细节。视频可在此处查看:https://stream.cadmore.media/r10.3171/2021.7.FOCVID21130 。