Muller Romain, Ebbo Mikael, Habert Paul, Torrents Julia, Gaubert Jean Yves, Schleinitz Nicolas
Internal Medicine Department Hopital La Timone, APHM, Aix Marseille University Marseille France.
Imaging Department Hopital Nord, APHM, Aix Marseille University Marseille France.
Respirol Case Rep. 2022 Nov 1;10(12):e01061. doi: 10.1002/rcr2.1061. eCollection 2022 Dec.
Pulmonary involvement of IgG4-associated disease is a rare condition with no codified treatment apart from steroid administration. We report here the case of a patient with pulmonary involvement of IgG4-RD successfully managed with Rituximab, in induction and maintenance therapy. This original case could support the use of Rituximab in rare situations of steroid-resistant or steroid-dependent pulmonary IgG4-RD.
IgG4相关性疾病的肺部受累是一种罕见病症,除了使用类固醇治疗外,尚无规范的治疗方法。我们在此报告一例IgG4相关性疾病肺部受累患者,通过使用利妥昔单抗进行诱导和维持治疗,获得了成功治疗。这一独特病例可为在类固醇抵抗或依赖的罕见肺部IgG4相关性疾病情况下使用利妥昔单抗提供依据。