Rawat Jiledar, Singh Sudhir, Pandey Anand, Singh Sarita
King George's Medical University, Lucknow, Uttar Pradesh, 226003, India.
King George's Medical University, Lucknow, Uttar Pradesh, 226003, India.
J Pediatr Surg. 2023 Feb;58(2):263-265. doi: 10.1016/j.jpedsurg.2022.10.036. Epub 2022 Oct 21.
Anterior urethral valves (AUVs) are rare congenital anomalies causing lower urinary tract obstruction in children. The present study highlights the clinical approach in identifying the condition and its treatment options.
Single centre, retrospective study of children.
Over a 16 year duration, 14 children were diagnosed with AUVs and diverticula with a mean age of 15 months. Clinical features included straining at micturation and a palpable penile swelling. Diagnosis was confirmed with voiding cystourethrogram and cystoscopy. An open surgical procedure was performed in 12 cases and endoscopic intervention done in one. On follow up 13 patients showed restoration of a normal voiding stream and normal renal function. One child died of chronic renal failure due to a delayed presentation, severe back-pressure changes, urinary ascites, and urosepsis. One patient developed a small urethrocutaneous fistula that healed spontaneously.
AUV, though rare, should be recognizable due to the combination of a poor urinary stream and visible swelling in the ventral aspect of penis. Open surgical excision is the method of choice, and the outcome is excellent.
Level IV.
前尿道瓣膜(AUVs)是导致儿童下尿路梗阻的罕见先天性异常。本研究重点介绍了识别该病症的临床方法及其治疗选择。
对儿童进行单中心回顾性研究。
在16年期间,14名儿童被诊断为AUVs和憩室,平均年龄为15个月。临床特征包括排尿时用力和可触及的阴茎肿胀。通过排尿性膀胱尿道造影和膀胱镜检查确诊。12例患者接受了开放手术,1例接受了内镜干预。随访时,13例患者排尿恢复正常,肾功能正常。1名儿童因就诊延迟、严重的背压改变、尿腹水和尿脓毒症死于慢性肾衰竭。1例患者出现小的尿道皮肤瘘,自行愈合。
AUV虽然罕见,但由于尿流不畅和阴茎腹侧可见肿胀的组合,应可识别。开放手术切除是首选方法,效果良好。
四级。