恶性肝脏血管周上皮样细胞瘤的临床诊断与治疗见解
Insights into clinical diagnosis and treatment of malignant hepatic perivascular epithelioid cell tumor.
作者信息
Li Zhongyu, Zhou Yongzhi, Wang Chaoqun, Yu Hongjun, Yang Guangchao, Ma Yong
机构信息
Key Laboratory of Hepatosplenic Surgery, Ministry of Education, Harbin, Heilongjiang, China.
Department of Minimal Invasive Hepatic Surgery, The First Affiliated Hospital of Harbin Medical University, Harbin, Heilongjiang, China.
出版信息
Intractable Rare Dis Res. 2022 Nov;11(4):202-205. doi: 10.5582/irdr.2022.01111.
Perivascular epithelioid cell tumors (PEComas) are infrequent mesenchymal tumors. They are usually benign, and only a few are malignant. These tumors are more commonly found in middle-aged women. PEComas are mainly composed of differentiated perivascular epithelioid cells arranged radially around the vascular cavity, and they are usually positive for melanocyte markers and smooth muscle cell differentiation markers. Among the PEComas, hepatic PEComas generally have no obvious symptoms and no typical imaging manifestations. Malignant hepatic PEComas are even rarer. So, we explained our insights into clinical diagnosis and treatment of malignant hepatic PEComas, in order to help clinicians and pathologists to further understand PEComas.
血管周上皮样细胞肿瘤（PEComas）是罕见的间叶性肿瘤。它们通常为良性，仅有少数为恶性。这些肿瘤更常见于中年女性。PEComas主要由围绕血管腔呈放射状排列的分化血管周上皮样细胞组成，并且通常对黑素细胞标志物和平滑肌细胞分化标志物呈阳性。在PEComas中，肝脏PEComas一般无明显症状，也无典型的影像学表现。恶性肝脏PEComas更为罕见。因此，我们阐述了对恶性肝脏PEComas临床诊断和治疗的见解，以帮助临床医生和病理学家进一步了解PEComas。
Zotero 插件