Endocrine Surgery Unit, Department of Surgery, Veneto Institute of Oncology, IOV-IRCCS, Via Gattamelata 64, 35128 Padua, Italy.
Department of Nuclear Medicine, Veneto Institute of Oncology, IOV-IRCCS, Via Gattamelata 64, 35128 Padua, Italy.
Medicina (Kaunas). 2023 Jan 11;59(1):149. doi: 10.3390/medicina59010149.
PEComa has become a widely accepted entity, and increased recognition has led to descriptions of this tumor in a wide variety of anatomic sites, including the adrenal gland. PEComa (perivascular epithelioid cell tumor) is a mesenchymal tumor composed of perivascular cells, and the most frequent sites of PEComas are the uterus and retroperitoneum. The incidence is <1 per 1,000,000 people. We report a case of adrenal metastatic PEComa in a 63-year-old man discovered by a spontaneous hematoma of the rectus abdominis. In our case, PEComa of the adrenal gland was a significant diagnostic dilemma as the morphologic and immunophenotypic features of this neoplasm may easily be confused with those of other more commonly encountered lesions.
PEComa 已被广泛认可，随着认识的提高，这种肿瘤在多种解剖部位的描述不断增加，包括肾上腺。PEComa（血管周上皮样细胞肿瘤）是一种由血管周细胞组成的间叶性肿瘤，PEComa 最常见的部位是子宫和腹膜后。发病率<1/100 万。我们报告了一例 63 岁男性的肾上腺转移性 PEComa，由腹直肌自发性血肿发现。在我们的病例中，肾上腺的 PEComa 是一个显著的诊断难题，因为这种肿瘤的形态和免疫表型特征很容易与其他更常见的病变混淆。
