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临床推理:一位 49 岁女性孤立性颅内窦硬膜动静脉瘘伴脊髓周围引流

Clinical Reasoning: A 49-Year-Old Woman With Isolated Sinus Intracranial Dural Arteriovenous Fistula With Perimedullary Drainage.

机构信息

From the Department of Neurology (H. Lu, H.-F.L.); Department of Neurosurgery (Y.M.), Xuanwu Hospital, Capital Medical University, Beijing; and Department of Neurology (H. Liu), The Affiliated Hospital of Chengde Medical College, Hebei, China.

出版信息

Neurology. 2023 May 9;100(19):921-926. doi: 10.1212/WNL.0000000000206824. Epub 2023 Jan 23.

DOI:10.1212/WNL.0000000000206824
PMID:36690454
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10186218/
Abstract

While demyelination is the most common etiology of longitudinally extensive myelopathy, other causes are important to recognize. In this study, we present the case of a longitudinal cervical lesion with a very rare cause. We discuss the approach to the differential diagnosis and workup for longitudinal myelopathy. This clinical reasoning case also illustrates the anatomical relationship between symptomatic spinal cord lesions and nonsymptomatic intracranial etiologies.

摘要

虽然脱髓鞘是长节段横贯性脊髓病最常见的病因,但其他原因也很重要。在本研究中,我们报告了一例非常罕见病因的纵向颈段病变。我们讨论了鉴别诊断和长节段脊髓病检查的方法。这个临床推理病例还说明了有症状的脊髓病变与无症状的颅内病因之间的解剖关系。

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J Neurointerv Surg. 2022 Jun;14(6):605-610. doi: 10.1136/neurintsurg-2021-017652. Epub 2021 Jun 3.
2
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J Stroke Cerebrovasc Dis. 2020 Aug;29(8):105007. doi: 10.1016/j.jstrokecerebrovasdis.2020.105007. Epub 2020 Jun 14.
3
Cervical Myelopathy Caused by Intracranial Dural Arteriovenous Fistula with Acute Worsening After Steroid Administration.颅内硬脑膜动静脉瘘所致的脊髓型颈椎病,在使用类固醇后急性加重
World Neurosurg. 2018 Dec;120:328-330. doi: 10.1016/j.wneu.2018.09.029. Epub 2018 Sep 12.
4
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J Clin Neurosci. 2016 Oct;32:61-6. doi: 10.1016/j.jocn.2015.12.048. Epub 2016 Aug 12.
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