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Contribution of the Interferon score in the management of an anti-NXP2 dermatomyositis patient with calcinosis successfully treated with tofacitinib.

作者信息

Robert Marie, Gallay Laure, Garnier Lorna, Pescarmona Rémi, Hot Arnaud

机构信息

Service de médecine interne et immunologie clinique, Centre Hospitalier Universitaire Edouard Herriot, Hospices Civils de Lyon, 5 Place d'Arsonval, 69437 Lyon, France.

Service de médecine interne et immunologie clinique, Centre Hospitalier Universitaire Edouard Herriot, Hospices Civils de Lyon, 5 Place d'Arsonval, 69437 Lyon, France.

出版信息

Joint Bone Spine. 2023 Jul;90(4):105532. doi: 10.1016/j.jbspin.2023.105532. Epub 2023 Jan 25.

DOI:10.1016/j.jbspin.2023.105532
PMID:36706944
Abstract
摘要

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Contribution of the Interferon score in the management of an anti-NXP2 dermatomyositis patient with calcinosis successfully treated with tofacitinib.干扰素评分在托法替布成功治疗的伴有钙质沉着的抗NXP2皮肌炎患者管理中的作用
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Calcinosis in juvenile dermatomyositis is influenced by both anti-NXP2 autoantibody status and age at disease onset.青少年皮肌炎中的钙质沉着受抗NXP2自身抗体状态和发病年龄的影响。
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Successful treatment of extensive calcifications and acute pulmonary involvement in dermatomyositis with the Janus-Kinase inhibitor tofacitinib - A report of two cases.成功治疗皮肌炎的广泛钙化和急性肺部受累:Janus 激酶抑制剂托法替布的疗效-两例报告。
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A striking treatment option for recalcitrant calcinosis in juvenile dermatomyositis: tofacitinib citrate.青少年皮肌炎中难治性钙质沉着症的一种显著治疗选择:枸橼酸托法替布。
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Profiling type I and II interferon responses reveals distinct subgroups of pediatric patients with autoinflammatory disorders.分析I型和II型干扰素反应可揭示患有自身炎症性疾病的儿科患者的不同亚组。
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Current evidence for janus kinase inhibitors in adult and juvenile dermatomyositis and key comparisons.成人及青少年皮肌炎中 Janus 激酶抑制剂的现有证据及关键比较。
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Calcinosis in dermatomyositis.
皮肌炎中的钙沉积。
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Tofacitinib for the treatment of severe rare skin diseases: a narrative review.托法替尼治疗严重罕见皮肤病:叙述性综述。
Eur J Clin Pharmacol. 2024 Apr;80(4):481-492. doi: 10.1007/s00228-024-03621-9. Epub 2024 Jan 17.