Falcini F, Bartolozzi G, Montanelli F, Pratesi G, Taccetti G, Tafi L, Volpi M, Lotti T
Dipartimento di Pediatria, Università degli Studi di Firenze, Italia.
Pediatr Med Chir. 1987 May-Jun;9(3):343-5.
The authors report a case of Mucha-Habermann disease in childhood. Mucha-Habermann disease is not a very well known, though not infrequent, disease. It is characterized by recurrent erythematous-papular-vesicular skin lesions associated with arthralgia or arthritis or large joints. Prognosis is generally favourable although an evolution towards Pityriasis Lichenoides Chronica and/or Mycosis Fungoides is possible. There are not specific laboratory findings for this form. Diagnosis is essentially based on histology showing an immunopathogenetic vasculitis. At the present time there is not a safe therapy for the disease; there are however indications for the use of Erythromycin and we followed these in our therapy with positive results.
作者报告了一例儿童期的穆查-哈伯曼病。穆查-哈伯曼病虽不罕见，但知名度不高。其特征为反复出现的红斑丘疹水疱性皮肤损害，伴有大关节的关节痛或关节炎。尽管有可能演变为慢性苔藓样糠疹和/或蕈样肉芽肿，但总体预后良好。这种类型没有特异性的实验室检查结果。诊断主要基于组织学显示的免疫病理发生性血管炎。目前尚无针对该疾病的安全疗法；不过有使用红霉素的指征，我们在治疗中遵循了这些指征，结果良好。
