Pison C, Levy P, Pin I, Blanc-Jouvan F, Wolf J E, Aguilaniu B, Paramelle B
Service de Pneumologie, CHU de Grenoble.
Rev Pneumol Clin. 1987;43(4):190-3.
Primary alveolar hypoventilation is a rare syndrome of unknown origin, characterized by a dysfunction of the automatic respiratory pattern in spite of normal lungs and in the absence of mechanical ventilatory defects. A reduction of the ventilatory response to CO2 is regularly found, and cardiac failure is common. The differential diagnosis mainly concerns the sleep apnoea syndrome. The usual treatments have little effectiveness.
原发性肺泡低通气是一种病因不明的罕见综合征，其特征是尽管肺部正常且不存在机械通气缺陷，但自主呼吸模式仍存在功能障碍。经常发现对二氧化碳的通气反应降低，且心力衰竭很常见。鉴别诊断主要涉及睡眠呼吸暂停综合征。常用治疗方法效果甚微。
