Bathla Sapna, Karim Wahaja, Kumar Anil, Bamba Charu
Department of Anesthesia, VMMC and Safdarjung Hospital, New Delhi, Delhi India.
Indian J Otolaryngol Head Neck Surg. 2022 Dec;74(Suppl 3):5225-5227. doi: 10.1007/s12070-020-01843-8. Epub 2020 Apr 16.
Fraser syndrome is a rare autosomal recessive disorder with spectrum of malformations. Gamut of abnormal airway includes high arched palate, laryngeal atresia, hypoplasia, laryngeal stenosis etc. Laryngeal intubation difficulties have often been reported in literature. Airway management and decision process leading to emergency tracheostomy in these children has been discussed.
弗雷泽综合征是一种罕见的常染色体隐性疾病,伴有一系列畸形。气道异常包括高拱腭、喉闭锁、发育不全、喉狭窄等。文献中经常报道这些患儿存在喉插管困难。本文讨论了这些儿童气道管理及导致紧急气管切开术的决策过程。