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一名26岁女性因波斯纳-施洛斯曼综合征继发非动脉炎性前部缺血性视神经病变。

Non-arteritic anterior ischemic optic neuropathy secondary to Posner-Schlossman syndrome in a twenty-six-year-old female.

作者信息

Schulte Alexandra, Skarf Barry, Monsalve Pedro

机构信息

Michigan State University Clinical Center, 804 Service Rd, East Lansing, MI, 48824, USA.

Henry Ford Health System, Ophthalmology Department, 2799 W. Grand Boulevard, Detroit, MI, 48202, USA.

出版信息

Am J Ophthalmol Case Rep. 2023 Feb 14;30:101816. doi: 10.1016/j.ajoc.2023.101816. eCollection 2023 Jun.

DOI:10.1016/j.ajoc.2023.101816
PMID:36865091
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9971115/
Abstract

PURPOSE

To describe a case of non-arteritic ischemic optic neuropathy (NAION) secondary to Posner-Schlossman syndrome in a twenty-six-year-old female.

OBSERVATIONS

A 26-year-old female presented with painful visual loss of the left eye, elevated intraocular pressure of 38 mmHg, and trace to 1+ anterior chamber cell. Diffuse optic disc edema in the left eye and a small cup-to-disc ratio of the right optic disc were evident. Magnetic resonance imaging was unremarkable.

CONCLUSIONS AND IMPORTANCE

The patient was diagnosed with NAION secondary to Posner-Schlossman syndrome, an uncommon ocular entity that can significantly affect vision. Posner-Schlossman syndrome can cause a decrease in ocular perfusion pressure involving the optic nerve and can lead to ischemia, swelling, and infarction. NAION should be considered in the differential diagnosis of young patients with sudden development of optic disc swelling and increased intraocular pressure with normal magnetic resonance imaging findings.

摘要

目的

描述一例26岁女性继发于波斯纳-施洛斯曼综合征的非动脉炎性缺血性视神经病变(NAION)。

观察结果

一名26岁女性出现左眼疼痛性视力丧失、眼压升高至38 mmHg,前房细胞微量至1+。左眼视盘弥漫性水肿,右眼视盘杯盘比小,这很明显。磁共振成像未见异常。

结论及重要性

该患者被诊断为继发于波斯纳-施洛斯曼综合征的NAION,这是一种罕见的眼部疾病,可显著影响视力。波斯纳-施洛斯曼综合征可导致涉及视神经的眼灌注压降低,并可导致缺血、肿胀和梗死。对于突然出现视盘肿胀、眼压升高且磁共振成像结果正常的年轻患者,鉴别诊断时应考虑NAION。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/0d38252379e0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/fbbaa6e340f7/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/002fc4fad448/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/a53ad235d66b/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/66f91cd6e72e/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/0d38252379e0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/fbbaa6e340f7/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/002fc4fad448/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/a53ad235d66b/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/66f91cd6e72e/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/96ac/9971115/0d38252379e0/gr5.jpg

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