Dash Sambit, Verma Neeta, Madavi Sheetal, Jadhav Jui A, Chandak Aruna
Department of Anesthesiology, Jawaharlal Nehru Medical College, Acharya Vinoba Bhave Rural Hospital, Datta Meghe Institute of Medical Sciences (Deemed University), Wardha, IND.
Cureus. 2023 Jan 30;15(1):e34406. doi: 10.7759/cureus.34406. eCollection 2023 Jan.
A patient diagnosed with facial plexiform neurofibromatosis type 1 who is 18 years old and is scheduled for tumour resection and debulking surgery of his face is the subject of this study. The purpose of this paper is to describe the anaesthetic treatment that was administered to this patient. In addition, we analyze the relevant literature, with a particular emphasis on the implications of modifying neurofibromatosis to achieve anaesthesia. Our patient was found to have multiple huge tumours all over his face. When he first arrived, he experienced cervical instability as a result of the enormous mass on the back of his head and in the region of his scalp. He also expected to have difficulty maintaining an airway and breathing through a bag and mask. To protect the patient's airway, a video laryngoscopy was performed, and a difficult airway cart was maintained on standby in the event it was required. In conclusion, the purpose of this case study was to demonstrate the relevance of comprehending the one-of-a-kind anaesthetic requirements of persons diagnosed with neurofibromatosis type 1 who are about to undergo surgical procedures. Neurofibromatosis is an extremely uncommon kind of disease that requires the anesthesiologist's undivided attention in surgical settings. Careful pre-operative planning and competent intra-operative treatment are required when dealing with patients who are expected to have difficult airway management.
本研究的对象是一名18岁、被诊断为1型面部丛状神经纤维瘤病且计划接受面部肿瘤切除和减容手术的患者。本文旨在描述对该患者实施的麻醉治疗。此外,我们分析了相关文献,特别强调了调整神经纤维瘤病以实现麻醉的影响。我们的患者被发现面部布满多个巨大肿瘤。他初到之时,由于后脑勺和头皮区域的巨大肿物,出现了颈椎不稳的情况。他还预计在通过面罩进行通气时维持气道和呼吸会有困难。为保护患者气道,进行了视频喉镜检查,并准备了困难气道推车以备不时之需。总之,本病例研究的目的是证明理解即将接受手术的1型神经纤维瘤病患者独特的麻醉需求的重要性。神经纤维瘤病是一种极为罕见的疾病,在手术环境中需要麻醉医生全神贯注。在处理预计气道管理困难的患者时,需要进行仔细的术前规划和有效的术中治疗。