Smaali Jihane, Charef Amal, Bamous Mehdi, Fatihi Jamal, Amezian Taoufik
Internal Medicine, Mohammed V Military Training Hospital, Rabat, MAR.
Faculty of Medicine and Pharmacy of Casablanca, Hassan II University, Casablanca, MAR.
Cureus. 2023 Feb 2;15(2):e34532. doi: 10.7759/cureus.34532. eCollection 2023 Feb.
Behçet's disease (BD) is a systemic vasculitis which is most often manifested by recurrent oral aphthosis, genital aphthosis, and ocular involvement with sometimes visceral damage, in particular neurological, digestive, vascular, or renal. We report the case of a 21-year-old man admitted for anasarca who revealed severe cardiac involvement associating endomyocardial fibrosis, intracardiac thrombi and involvement of the tricuspid valve in the context of BD diagnosed a posteriori. Cardiac involvement is exceptional during BD, especially as a mode of entry into the disease. It can be particularly severe, hence the need for early diagnosis, rapid and sometimes aggressive management. Close monitoring is also necessary in order to watch for the occurrence of visceral manifestations, particularly in young patients.
白塞病(BD)是一种全身性血管炎,最常见的表现为复发性口腔溃疡、生殖器溃疡,以及眼部受累,有时还会出现内脏损害,特别是神经、消化、血管或肾脏方面的损害。我们报告了一例21岁因全身性水肿入院的男性病例,该病例在事后诊断为白塞病的情况下,显示出严重的心脏受累,伴有心内膜纤维化、心内血栓形成和三尖瓣受累。心脏受累在白塞病中较为罕见,尤其是作为疾病的首发表现。它可能特别严重,因此需要早期诊断、快速且有时积极的治疗。密切监测也很有必要,以便观察内脏表现的发生,尤其是在年轻患者中。