Skillington P D, Brawn W J, Edis B D, Menahem S, Venables A W, Goh T H, Mee R B
Royal Children's Hospital, Parkville, Victoria, Australia.
Aust N Z J Surg. 1987 Sep;57(9):599-604. doi: 10.1111/j.1445-2197.1987.tb01433.x.
Six cases of primary cardiac tumour have been operated upon in a 7 year period from 1 June 1979 until 1 June 1986. All patients were under 6 months of age at the time of operation and two of the patients were in their first week of life. The principal indication for surgery was obstruction mainly at the right or left ventricular outflow tract level. More recently echo evaluation alone has been adequate to define the problem prior to surgery. Surgical excision has been performed without mortality or significant complications. In most cases resection has been complete, although in one case residual tumour has been left because of attachment of the tumour to vital structures. Follow-up of this case has not resulted in further surgery being required because of regrowth of the tumour. In one case, with co-existent congenital heart disease, the tumour was brought to notice after palliative systemic to pulmonary artery shunt had been performed. From the cardiac view point gratifying results have been obtained both in the short and long term following surgical resection. However, for patients with rhabdomyoma, later development of symptomatic tuberosclerosis should be anticipated in 50% of cases.
从1979年6月1日至1986年6月1日的7年期间，共对6例原发性心脏肿瘤患者进行了手术。所有患者在手术时均未满6个月，其中2例患者为出生后第一周。手术的主要指征是梗阻，主要发生在右或左心室流出道水平。最近，仅通过超声评估就足以在手术前明确问题。手术切除未导致死亡或严重并发症。在大多数情况下，切除是彻底的，尽管有1例因肿瘤附着于重要结构而残留了部分肿瘤。对该病例的随访未因肿瘤复发而需要进一步手术。有1例患者同时患有先天性心脏病，在进行姑息性体肺分流术后发现了肿瘤。从心脏角度来看，手术切除后短期和长期均取得了令人满意的结果。然而，对于患有横纹肌瘤的患者，预计50%的病例会在后期出现有症状的结节性硬化症。
