Nusbaum Lee, Paul Michael, Maharshak Idit
Azrieli Faculty of Medicine, Bar-Ilan University, Israel.
Department of Ophthalmology, Edith Wolfson Medical Center, Israel, Sackler Faculty of Medicine, Tel-Aviv University, Israel.
Harefuah. 2023 Feb;162(2):98-102.
Orbital dermoid cysts are benign choristomas that arise from the entrapment of ectodermal elements adjacent to the fetal bony suture lines. They are considered congenital, but not all are diagnosed at birth. They are the most common orbital tumors in children. While superficial dermoid cysts appear early in life, deep dermoid cysts remain clinically occult until adolescence or adulthood, when they enlarge and may cause proptosis, ocular and orbital symptoms, and even neurological symptoms. In addition, many deep orbital dermoid cysts present with chronic inflammation resulting from lipid leakage from the cysts. They pose a diagnostic and therapeutic challenge, require radiological imaging for planning the surgical approach and may be difficult to remove. Early diagnosis and complete surgical removal of the cysts are the recommended therapeutic approach. In this paper, we present a literature review of deep orbital dermoid cysts to provide useful guidance for their diagnosis and management.
眼眶皮样囊肿是一种良性迷离瘤,由胎儿骨缝线附近的外胚层成分被困所致。它们被认为是先天性的,但并非所有在出生时就被诊断出来。它们是儿童最常见的眼眶肿瘤。浅表性皮样囊肿在生命早期出现,而深部皮样囊肿在临床上一直隐匿,直到青春期或成年期才会增大,并可能导致眼球突出、眼部和眼眶症状,甚至神经症状。此外,许多深部眼眶皮样囊肿会因囊肿内脂质泄漏而出现慢性炎症。它们带来了诊断和治疗方面的挑战,需要进行放射影像学检查以规划手术入路,且可能难以切除。早期诊断并完整切除囊肿是推荐的治疗方法。在本文中,我们对深部眼眶皮样囊肿进行文献综述,为其诊断和管理提供有用的指导。