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一名成年斯蒂尔病患者获得性甲型血友病:类固醇治疗成功

Acquired hemophilia A in a patient with adult-onset Still's disease: Successful treatment with steroids.

作者信息

Chebbi Donia, Marzouk Sameh, Krichen Imen, El Ahmer Ikram, Snoussi Mouna, Dammak Chifa, Frikha Faten, Salah Raida Ben, Kallel Choumous, Bahloul Zouhir

机构信息

Department of Internal Medicine Hedi Chaker University Hospital Sfax Tunisia.

Department of Hematology Habib Bourguiba University Hospital Sfax Tunisia.

出版信息

Clin Case Rep. 2023 Mar 14;11(3):e7105. doi: 10.1002/ccr3.7105. eCollection 2023 Mar.

Abstract

Acquired hemophilia A (AHA) is a potentially life-threatening hemorrhagic disorder with many etiologies. We report the first case in the literature describing the association of AHA with adult-onset Still's disease (AOSD).

摘要

获得性血友病A(AHA)是一种病因多样、可能危及生命的出血性疾病。我们报告了文献中首例描述AHA与成人斯蒂尔病(AOSD)关联的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3d5a/10014520/c9c372b86fcf/CCR3-11-e7105-g003.jpg

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