Department of Diagnostic Imaging, Instituto Nacional de Salud del Niño San Borja, Av. Javier Prado Este 3101, 15037, Lima, Peru.
Department of Diagnostic Imaging, Hospital Luis Negreiros Vega, Av. Tomas Valle 3535, 07036, Lima, Peru.
Pediatr Radiol. 2023 Jul;53(8):1698-1703. doi: 10.1007/s00247-023-05605-w. Epub 2023 Mar 21.
Primary intracranial sarcoma is a very rare high-grade tumor. Scant reports exist on this malignancy in children, which limit the information about its imaging characteristics.
We aimed to describe the main characteristics of primary intracranial sarcoma on MRI.
In this cross-sectional descriptive observational study, we reviewed 18 patients (aged 1-18 years) with primary intracranial sarcomas diagnosed between 2015 and 2021.
The main findings were contrast enhancement (100%), diffusion restriction (78%), hemorrhage (89%), meningeal extension (67%), necrosis (67%), and supratentorial location (72%).
Primary intracranial sarcoma are typically supratentorial in location. MRI findings of primary intracranial sarcoma are similar to other intracranial malignancies.
原发性颅内肉瘤是一种非常罕见的高级别肿瘤。关于儿童的这种恶性肿瘤的报道很少,这限制了其影像学特征的信息。
我们旨在描述原发性颅内肉瘤的主要 MRI 特征。
在这项横断面描述性观察研究中,我们回顾了 2015 年至 2021 年间诊断的 18 例(年龄 1-18 岁)原发性颅内肉瘤患者。
主要发现包括增强(100%)、弥散受限(78%)、出血(89%)、脑膜延伸(67%)、坏死(67%)和幕上位置(72%)。
原发性颅内肉瘤通常位于幕上。原发性颅内肉瘤的 MRI 表现与其他颅内恶性肿瘤相似。