Loureiro Marcelo de Paula, Novais Pietro Maran, Paulin João Augusto Nocera, de Almeida Daniel Benzecry, de Lemos Arlindo Nascimento
Universidade Positivo - UP, Curitiba, PR, Brasil.
Instituto Jacques Perissat de Cirurgia Minimamente Invasiva - IJP, Curitiba, PR, Brasil.
J Vasc Bras. 2023 Mar 10;22:e20220095. doi: 10.1590/1677-5449.202200952. eCollection 2023.
Erythromelalgia is a rare disease, involving pain, edema, redness, and hyperthermia in the limbs. It is extremely refractory to drugs, has no defined treatment, and causes psychological comorbidities in the patient. We describe a case of erythromelalgia involving a 17-year-old boy who had been suffering from the disease for almost 4 years prior to finding an effective treatment. A bilateral endoscopic lumbar sympathectomy was performed, limited to L2 and L3 resections. Four weeks after the procedure, the patient's symptoms were significantly mitigated and at 8 months follow-up he remained almost asymptomatic. Endoscopic lumbar sympathectomy was an effective treatment for primary erythromelalgia in this teenager, with exceptional reduction of his symptoms.
红斑性肢痛症是一种罕见疾病，累及四肢疼痛、水肿、发红及体温过高。它对药物治疗极难奏效，没有明确的治疗方法，且会导致患者出现心理合并症。我们描述了一例红斑性肢痛症病例，患者为一名17岁男孩，在找到有效治疗方法之前，他已患病近4年。实施了双侧内镜下腰交感神经切除术，仅限于L2和L3节段切除。术后四周，患者症状明显减轻，随访8个月时他几乎无症状。内镜下腰交感神经切除术对这名青少年的原发性红斑性肢痛症是一种有效的治疗方法，其症状得到了显著缓解。
