Department of Respiratory Medicine, Nagano Matsushiro General Hospital, Nagano, Japan.
Department of Hematology and Medical Oncology, Shinshu University Graduate School of Medicine School of Medicine, Nagano, Japan.
Thorac Cancer. 2023 May;14(13):1204-1207. doi: 10.1111/1759-7714.14855. Epub 2023 Mar 25.
Here, we report a case of mediastinal mesenchymal tumor with a pericytic neoplasm feature that responded to radiation therapy. A 43-year-old man visited our hospital with a complaint of esophageal obstruction and chest pain. Chest computed tomography revealed a middle mediastinal tumor and a mesenchymal tumor was diagnosed with a pericytic neoplasm feature by video-assisted thoracoscopic biopsy. The definitive treatment for soft tissue tumor is surgical resection; however, the mediastinal tumor was unresectable because of esophageal and tracheal invasion. Radiation therapy was administered and there was a partial tumor response and 2 years disease-free status. With a review of the literature, we discuss the clinical and pathological characteristics of this rare tumor and its treatment.
在这里,我们报告了一例纵隔间叶性肿瘤,具有血管周细胞瘤特征,对放射治疗有反应。一名 43 岁男性因食管梗阻和胸痛就诊于我院。胸部计算机断层扫描显示纵隔中部肿瘤,通过电视辅助胸腔镜活检诊断为具有血管周细胞瘤特征的间叶性肿瘤。软组织肿瘤的确定性治疗是手术切除;然而,由于食管和气管侵犯,纵隔肿瘤无法切除。给予放射治疗,肿瘤部分缓解,无疾病状态持续 2 年。通过文献复习,我们讨论了这种罕见肿瘤的临床和病理特征及其治疗方法。