单侧视网膜血管炎作为帕里-罗姆伯格综合征（进行性半侧面部萎缩）的首发表现
Unilateral Retinal Vasculitis as the Presenting Manifestation of Parry-Romberg Syndrome (Progressive Hemifacial Atrophy).
作者信息
Atchison Elizabeth A, Szewka Aimee J, Merrill Pauline T
机构信息
Ophthalmology Ltd, Sioux Falls, SD, USA.
Department of Ophthalmology, Rush Medical College, Rush University, Chicago, IL, USA.
出版信息
J Vitreoretin Dis. 2021 May 21;6(5):409-411. doi: 10.1177/24741264211015538. eCollection 2022 Sep-Oct.
PURPOSE
This work aims to present a case of retinal vasculitis associated with Parry-Romberg syndrome.
METHOD
A case report is presented.
RESULTS
A 17-year-old man with new floaters was found to have 20/40 vision with 1+ vitreous cell and retinal vasculitis in the right eye only. Workup for infectious etiologies did not reveal an explanation for the retinal vasculitis. However, magnetic resonance imaging of the head showed areas of linear band-like atrophy and scarring of the scalp and soft tissues as well as areas of gliosis and encephalomalacia in the subcortical white matter, all of which were consistent with Parry-Romberg syndrome. The patient was prescribed oral steroids and methotrexate, and the retinal vasculitis improved.
CONCLUSIONS
Parry-Romberg syndrome is a rarely reported cause of retinal vasculitis and should be kept in the differential for retinal vasculitis.
目的
本研究旨在报告一例与帕里-龙贝格综合征相关的视网膜血管炎病例。
方法
本文呈现了一例病例报告。
结果
一名17岁男性因新发飞蚊症就诊，右眼视力为20/40，有1+玻璃体细胞及视网膜血管炎，左眼未见异常。针对感染性病因的检查未发现视网膜血管炎的病因。然而，头部磁共振成像显示头皮和软组织存在线性带状萎缩和瘢痕形成区域，以及皮质下白质的胶质增生和脑软化区域，所有这些均符合帕里-龙贝格综合征。该患者接受了口服类固醇和甲氨蝶呤治疗，视网膜血管炎有所改善。
结论
帕里-龙贝格综合征是一种罕见的视网膜血管炎病因，在诊断视网膜血管炎时应考虑到该疾病。
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