Tazelaar H D, Moore G W, Hutchins G M
Pediatr Cardiol. 1986;6(4):187-91. doi: 10.1007/BF02310996.
Five patients with ventricular inversion, corrected transposition of the great arteries, and atresia of the left-sided atrioventricular (tricuspid) valve have been observed. Three patients died in infancy, two had large interatrial communications, one with an early stage of arterial-type hypertensive pulmonary vascular disease, and the third patient had a very small interatrial communication and severe cyanosis. The other two patients survived into adulthood; both had small interatrial communications, and one had severe venous-type hypertensive pulmonary vascular disease. The longer survival of the two patients is attributed to a balance between resistance and blood flow in the pulmonary circulation influenced by the size of the interatrial communication.
已观察到5例心室反位、大动脉转位矫正型及左侧房室(三尖瓣)闭锁的患者。3例患者在婴儿期死亡,2例有较大的房间隔交通,其中1例处于动脉型高血压性肺血管疾病早期,第3例患者房间隔交通非常小且有严重紫绀。另外2例患者存活至成年;二者均有小的房间隔交通,其中1例有严重的静脉型高血压性肺血管疾病。这2例患者存活时间较长归因于房间隔交通大小对肺循环中阻力与血流之间平衡的影响。