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使用医生改良型移植物治疗合并迷走右锁骨下动脉的巨大胸腹主动脉瘤。

Treating a Large Thoracoabdominal Aneurysm With Aberrant Right Subclavian Artery With a Physician-Modified Graft.

作者信息

Rosu Cristian, Charbonneau Philippe, Drudi Laura M, Blair Jean-François, Beaudoin Nathalie, Elkouri Stéphane

机构信息

Division of Vascular Surgery, Centre Hospitalier de l'Université de Montréal, Montreal, QC, Canada.

Carrefour de l'Innovation, Centre de Recherche, Centre Hospitalier de l'Université de Montréal, Montreal, QC, Canada.

出版信息

J Endovasc Ther. 2025 Feb;32(1):251-258. doi: 10.1177/15266028231166291. Epub 2023 Apr 21.

DOI:10.1177/15266028231166291
PMID:37086014
Abstract

Large thoracoabdominal aortic aneurysms due to chronic aortic dissection in patients with connective tissue disorders such as Loeys-Dietz syndrome present a challenging scenario, particularly in cases of variant anatomy and when patients are not candidates for conventional open repair. We demonstrate how by combining and modifying off-the-shelf devices during a hybrid procedure, one can create an endovascular solution tailored to the patient's complex anatomy, making use of an aberrant right subclavian artery, and allow for good clinical outcomes.

摘要

对于患有诸如洛伊迪茨综合征等结缔组织疾病的患者,由慢性主动脉夹层引起的大型胸腹主动脉瘤是一个具有挑战性的情况,特别是在解剖结构变异以及患者不适合传统开放修复的病例中。我们展示了在杂交手术过程中如何通过组合和修改现成的装置,利用异常的右锁骨下动脉,为患者复杂的解剖结构量身定制一种血管内解决方案,并实现良好的临床效果。

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