A recurrent pleuropneumonia revealing Erdheim-Chester Disease.
作者信息
Kherabi Yousra, Chazal Thibaud, Emile Jean-François, Allaham Wassim, Mallart Elise, de Lastours Victoire, Haroche Julien, Nguyen Yann
机构信息
Service de Médecine Interne, AP-HP.Nord, Hôpital Beaujon, Université Paris Cité, Clichy, France.
Service de Médecine Interne 2, Institut E3M, Inserm UMRS, Centre D'Immunologie et des Maladies Infectieuses (CIMI-Paris), Assistance Publique-Hôpitaux de Paris (APHP), Groupement Hospitalier Pitié-Salpêtrière, Sorbonne Université, Paris, France.
出版信息
Respir Med Case Rep. 2023 Apr 7;43:101843. doi: 10.1016/j.rmcr.2023.101843. eCollection 2023.
Erdheim-Chester disease (ECD) is a rare form of L group histiocytosis, accounting for up to 1500 cases to date worldwide, which mainly affects men between their 5th and 7th decade of life. The most frequent manifestations are bone involvement, perirenal infiltration with an evocating appearance of "hairy kidneys", and a "coated aorta" aspect. Lung involvement in ECD is less common and includes pleural infiltration and interstitial lung disease. Herein, we report the case of a 76-year-old woman with recurrent pleuropneumonia revealing ECD.
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