Gugliantini P, Rosati D, Pilato B G, de Zorzi A
Radiol Med. 1986 Apr;72(4):173-9.
In 3 cases of Cooley's anemia rib notchings were found. In the first case the clinical pattern did not allow to exclude postductal type of aortic coarctation and thus was performed a venous digital aortography (SVC) showing the integrity of the aortic arch and the absence of intercostal arterial collateral circulation. Only two previous descriptions of rib notchings in thalassemia were found in literature, and the authors shortly describe the 3 observed cases and suggest some possible pathogenetic interpretations either of rib notchings in thalassemia or of the relatively late appearance (adolescence) of rib notchings.
在3例库利贫血患者中发现了肋骨切迹。在第一例中，临床表现无法排除动脉导管后型主动脉缩窄，因此进行了静脉数字主动脉造影（上腔静脉），显示主动脉弓完整且无肋间动脉侧支循环。文献中仅发现两篇关于地中海贫血中肋骨切迹的描述，作者简要描述了观察到的3例病例，并对地中海贫血中肋骨切迹或肋骨切迹相对较晚出现（青春期）提出了一些可能的发病机制解释。
