Ait M'barek Yassine, Hamadi Hajar, Benantar Lamia, Hamidi Elmehdi, Aniba Khalid
Neurological Surgery, Ibn Tofail Hospital, Mohammed VI University Hospital, Marrakech, MAR.
Cureus. 2023 Apr 8;15(4):e37302. doi: 10.7759/cureus.37302. eCollection 2023 Apr.
Congenital factor V deficiency (FVD) is a rare bleeding disorder due to an inherited mutation. So far, there are no standard protocols for pre- and peri-operative management of patients with factor V deficiency. This poses a challenge for surgeons and requires a multidisciplinary approach. We present a case of a 60-year-old woman with factor V deficiency admitted to the neurosurgery department of Ibn Tofail Hospital for hydrocephalus requiring a ventriculoperitoneal shunt. Pre-operative management of the patients as well as outcome and follow-up are described and compared with relevant literature.
先天性因子V缺乏症（FVD）是一种由于遗传突变引起的罕见出血性疾病。到目前为止，对于因子V缺乏症患者的术前和围手术期管理尚无标准方案。这给外科医生带来了挑战，需要多学科方法。我们报告一例60岁患有因子V缺乏症的女性患者，因脑积水入住伊本·图菲勒医院神经外科，需要进行脑室腹腔分流术。描述了该患者的术前管理以及结果和随访情况，并与相关文献进行了比较。
