From the Division of Plastic and Reconstructive Surgery, Department of Surgery, Washington University School of Medicine.
Department of Neurosurgery, Johns Hopkins All Children's Hospital.
Plast Reconstr Surg. 2024 May 1;153(5):984e-987e. doi: 10.1097/PRS.0000000000010685. Epub 2023 May 16.
Premature fusion of the lambdoid suture is the most uncommon single-suture synostosis. It presents with a classic "windswept" appearance, a trapezoid-shaped head, and significant skull asymmetry notable for an ipsilateral mastoid bulge and contralateral frontal bossing. Because of the rarity of lambdoid synostosis, little is known about optimal techniques for its treatment. In particular, the proximity of the lambdoid suture to critical intracranial structures such as the superior sagittal and transverse sinuses represents a potential for significant intraoperative bleeding. Prior work has shown that parietal asymmetry persists after repair in these cases. In this article, the authors present a technique for the treatment of unilateral lambdoid craniosynostosis along with two representative cases. This calvarial vault remodeling technique requires the removal of both ipsilateral and contralateral parietal bones. These are moved across hemispheres and reinset on opposite sides to help correct the parietal asymmetry. Obliquely orientated barrel stave osteotomies are performed to provide a safe mechanism for correction of occipital flattening. The authors' early results show improvement in correction of volume asymmetry 1 year postoperatively relative to patients treated with prior calvarial vault remodeling techniques. The authors believe the technique presented here corrects the windswept appearance in patients with lambdoid craniosynostosis and also reduces the potential for complications. Further work will be necessary to confirm this technique's long-term efficacy in a larger cohort.
矢状缝过早融合是最不常见的单一颅缝融合。它表现出典型的“横扫”外观、梯形头部和明显的颅骨不对称,表现为同侧乳突突出和对侧额骨突出。由于矢状缝融合的罕见性,对于其治疗的最佳技术知之甚少。特别是,矢状缝与上矢状窦和横窦等关键颅内结构的接近,代表了术中大量出血的潜在风险。先前的工作表明,在这些情况下,修补后顶骨不对称仍然存在。在本文中,作者介绍了一种治疗单侧矢状缝颅缝早闭的技术,并提供了两个代表性病例。这种颅顶穹窿重塑技术需要切除同侧和对侧顶骨。将这些骨片移到对侧半球并重新固定在对侧,以帮助纠正顶骨不对称。斜向的桶状骨切开术用于提供安全的矫正枕骨扁平的机制。作者的早期结果显示,与接受先前颅顶穹窿重塑技术治疗的患者相比,术后 1 年体积不对称的矫正得到了改善。作者认为,这里介绍的技术可以纠正矢状缝颅缝早闭患者的横扫外观,并降低并发症的风险。需要进一步的工作来确认这种技术在更大队列中的长期疗效。