Moreno Sánchez Amelia, Molina Herranz David, Sánchez Andrés Armando, Monge Galindo Lorena
Servicio de Pediatría. Sección de Neuropediatría. Hospital Universitario Miguel Servet..
Sección de Neuropediatría. Hospital Infantil Universitario Miguel Servet. Zaragoza. España.
An Sist Sanit Navar. 2023 Apr 25;46(1):e1031. doi: 10.23938/ASSN.1031.
Intracranial hypotension syndrome (IHS) is attributed to reduced cerebrospinal fluid (CSF) pressure. It may be spontaneous or secondary to a history of trauma or systemic disease. We present the case of an 11-year-old boy, with medical history of Marfan syndrome, with orthostatic headache and persistent vomiting (12 hours) following a fall on the sacrococcygeal region. Magnetic resonance showed extradural fluid collections at dorsal and lumbosacral levels, compatible with CSF leak. The condition was resolved with treatment, but the patient had two new episodes during the follow-up period. Thus, an epidural blood patch was performed two years after the first episode. Although HIS is uncommon in children, it should be suspected in patients with orthostatic headache, particularly if the patient presents a connectivopathy. Few studies have assessed the management of HIS in paediatric age. The case presented here and the reviewed available literature provides further data for these type of cases.
颅内低压综合征（IHS）归因于脑脊液（CSF）压力降低。它可能是自发性的，也可能继发于外伤史或全身性疾病。我们报告一例11岁男孩的病例，该男孩有马凡综合征病史，在骶尾部跌倒后出现体位性头痛和持续呕吐（12小时）。磁共振成像显示在背侧和腰骶部水平有硬膜外液体积聚，符合脑脊液漏。经治疗病情得到缓解，但患者在随访期间又出现了两次新发作。因此，在首次发作两年后进行了硬膜外血贴疗法。虽然IHS在儿童中并不常见，但对于体位性头痛的患者应怀疑此病，特别是如果患者存在结缔组织病。很少有研究评估儿童期IHS的治疗。这里呈现的病例以及所回顾的现有文献为这类病例提供了更多数据。
